Ornithine Carbamoyltransferase Rabbit Monoclonal Antibody

Ornithine Carbamoyltransferase Rabbit Monoclonal Antibody

Cat: AMRe87448
Boyut:50μL Fiyat:$168_x000D_
Boyut:100μL Fiyat:$300_x000D_
Uygulama:WB,IHC,IP
Reaktivite:Human,Mouse,Rat
Konjuge:Unconjugated
İsteğe bağlı konjugeler: Biotin, FITC (ücretsiz). Diğer 26 konjugatı görün.

Gen Adı:Ornithine Carbamoyltransferase
Category: 組換えモノクローナル抗体 Tags: , , , , , , , ,
Ornithine Carbamoyltransferase Rabbit Monoclonal Antibody
Konjugasyon: Unconjugated
Recombinant rabbit monoclonal antibody
Uygulama
IHC  ICC/IF  ELISA WB,IHC,IP
Reaktivite
Human,Mouse,Rat
Gen Adı
Ornithine Carbamoyltransferase
Saklama
Aliquot and store at -20°C (valid for 12 months). Avoid freeze/thaw cycles.
Özet
Ürün Adı Ornithine Carbamoyltransferase Rabbit Monoclonal Antibody
Açıklama Recombinant rabbit monoclonal antibody
Konak Rabbit
Reaktivite Human,Mouse,Rat
Konjugasyon Unconjugated
Modifikasyon Unmodified
İzotip IgG
Klonalite Monoclonal
Form Liquid
Konsantrasyon Unconjugated
Saklama Aliquot and store at -20°C (valid for 12 months). Avoid freeze/thaw cycles.
Nakliye Ice bags.
Tampon Supplied in 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% sodium azide and 0.05% protective protein. Stable for 12 months from date of receipt.
Saflaştırma Affinity Purification
Antijen Bilgisi
Gen Adı Ornithine Carbamoyltransferase
Alternatif İsimler OCTD
Gen Kimliği 5009
SwissProt Kimliği P00480
İmmünojen A synthetic peptide of human Ornithine Carbamoyltransferase
Uygulama
Uygulama WB,IHC,IP
Seyreltme Oranı WB 1:500-1:2000,IHC 1:50-1:200,IP 1:20-1:50
Moleküler Ağırlık Calculated MW:40 kDa; Observed MW:40 kDa
Araştırma Alanı
Arka Plan
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. [provided by RefSeq, Jul 2008]
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