Galactosidase alpha Rabbit Monoclonal Antibody

Galactosidase alpha Rabbit Monoclonal Antibody

Cat: AMRe85595
Boyut:50μL Fiyat:$168_x000D_
Boyut:100μL Fiyat:$300_x000D_
Uygulama:WB,IHC,IP
Reaktivite:Human
Konjuge:Unconjugated
İsteğe bağlı konjugeler: Biotin, FITC (ücretsiz). Diğer 26 konjugatı görün.

Gen Adı:Galactosidase alpha
Category: 組換えモノクローナル抗体 Tags: , , , , , ,
Galactosidase alpha Rabbit Monoclonal Antibody
Konjugasyon: Unconjugated
Recombinant rabbit monoclonal antibody
Uygulama
IHC  ICC/IF  ELISA WB,IHC,IP
Reaktivite
Human
Gen Adı
Galactosidase alpha
Saklama
Aliquot and store at -20°C (valid for 12 months). Avoid freeze/thaw cycles.
Özet
Ürün Adı Galactosidase alpha Rabbit Monoclonal Antibody
Açıklama Recombinant rabbit monoclonal antibody
Konak Rabbit
Reaktivite Human
Konjugasyon Unconjugated
Modifikasyon Unmodified
İzotip IgG
Klonalite Monoclonal
Form Liquid
Konsantrasyon Unconjugated
Saklama Aliquot and store at -20°C (valid for 12 months). Avoid freeze/thaw cycles.
Nakliye Ice bags.
Tampon Purified antibody in TBS with 0.05% sodium azide,0.05%protective protein and 50% glycerol.
Saflaştırma Affinity Purification
Antijen Bilgisi
Gen Adı Galactosidase alpha
Alternatif İsimler Alpha gal A; GALA; Galactosidase; alpha; GLA; Melibiase
Gen Kimliği 2717
SwissProt Kimliği P06280
İmmünojen A synthetic peptide of human Galactosidase alpha
Uygulama
Uygulama WB,IHC,IP
Seyreltme Oranı WB 1:500-1:1000,IHC 1:50-1:100,IP 1:10-1:20
Moleküler Ağırlık Calculated MW: 49 kDa; Observed MW: 49 kDa
Araştırma Alanı
Arka Plan
Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.
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