Acid sphingomyelinase Rabbit Monoclonal Antibody

Acid sphingomyelinase Rabbit Monoclonal Antibody

Cat: AMRe87490
Boyut:50μL Fiyat:$168_x000D_
Boyut:100μL Fiyat:$300_x000D_
Uygulama:WB
Reaktivite:Human
Konjuge:Unconjugated
İsteğe bağlı konjugeler: Biotin, FITC (ücretsiz). Diğer 26 konjugatı görün.

Gen Adı:Acid sphingomyelinase
Category: 組換えモノクローナル抗体 Tags: , , , ,
Acid sphingomyelinase Rabbit Monoclonal Antibody
Konjugasyon: Unconjugated
Recombinant rabbit monoclonal antibody
Uygulama
IHC  ICC/IF  ELISA WB
Reaktivite
Human
Gen Adı
Acid sphingomyelinase
Saklama
Aliquot and store at -20°C (valid for 12 months). Avoid freeze/thaw cycles.
Özet
Ürün Adı Acid sphingomyelinase Rabbit Monoclonal Antibody
Açıklama Recombinant rabbit monoclonal antibody
Konak Rabbit
Reaktivite Human
Konjugasyon Unconjugated
Modifikasyon Unmodified
İzotip IgG
Klonalite Monoclonal
Form Liquid
Konsantrasyon Unconjugated
Saklama Aliquot and store at -20°C (valid for 12 months). Avoid freeze/thaw cycles.
Nakliye Ice bags.
Tampon Supplied in 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% sodium azide and 0.05% protective protein. Stable for 12 months from date of receipt.
Saflaştırma Affinity Purification
Antijen Bilgisi
Gen Adı Acid sphingomyelinase
Alternatif İsimler ASM; NPD; ASMASE
Gen Kimliği 6609
SwissProt Kimliği P17405
İmmünojen Recombinant protein of human Acid sphingomyelinase
Uygulama
Uygulama WB
Seyreltme Oranı WB 1:500-1:2000
Moleküler Ağırlık Calculated MW:70 kDa; Observed MW:70 kDa
Araştırma Alanı
Arka Plan
The protein encoded by this gene is a lysosomal acid sphingomyelinase that converts sphingomyelin to ceramide. The encoded protein also has phospholipase C activity. Defects in this gene are a cause of Niemann-Pick disease type A (NPA) and Niemann-Pick disease type B (NPB). Multiple transcript variants encoding different isoforms have been identified. [provided by RefSeq, Jul 2010]
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